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Carglumic Acid (D58205)  
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100mg/468.00元
1g/1540.00元
大包裝/詢價(jià)
產(chǎn)品編號(hào) D58205
英文名稱 Carglumic Acid
中文名稱 氨甲酰谷氨酸
別    名 Carbaglu; Carglumic Acid; N-Carbamyl-L-glutamic acid; Carbamylglutamic acid; Carbamino-L-glutamic acid; Ureidoglutaric acid; N-Carbamylglutamate  
克 隆 號(hào)
CAS 1188-38-1
理論分子量 190.15 kDa
檢測(cè)分子量
保存條件 Powder: -20℃ for 3 years | In solvent: -80℃ for 1 year
注意事項(xiàng) This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
產(chǎn)品介紹 Carglumic acid is an orphan drug used to treat hyperammonemia in patients with N-acetyl glutamate synthase absence. This rare hereditary disease results in elevated blood levels of ammonia, which can eventually cross the blood-brain barrier and lead to neurologic problems, coma, cerebral edema, and death. Carglumic acid was approved by the U.S. FDA on 18 March 2010.

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